SJOGRENS OR DRY MOUTH & DRY EYES
The Mount Sinai
Medical Center
New York, New York 10029
February 2000
17) If you have diseases such as gerd,
sojgrens, arthritis etc., that seem to be triggered with the onset of PBC,
do they go away or diminish after transplant?
Answer
To the extent that certain diseases associated with PBC would respond to the immunosuppression used after a transplant, some symptoms might resolve. For example, if one had rheumatoid arthritis, prednisone used after the transplant might ameliorate some symptoms. Gastroesophageal reflux disease (GERD) is not linked to PBC and would probably not resolve after transplant. I don't think anyone has looked specifically at Sjogrens syndrome; perhaps we should. I would guess the symptoms would not change since diseases associated with PBC are just that, associated but not caused by PBC, and they tend to run their own courses.
Thomas
Shaw-Stiffel, MD,
Medical
Director,
Living
Donor Liver Transplantation
Univ.
of Pittsburgh
Medical
Center - Presbyterian Hospital Center for Liver Diseases
March
2003
Question 5
In
your experience, what are the most common autoimmune diseases associated
with PBC?
Answer 5
The
top is thyroid, then come Sjogren's (dry eyes and mouth), scleroderma (part
of systemic sclerosis with bound-down skin in the hands and face,
hyerpigmentation and skin lesions called telangiectasias, discrete from the
"spiders" seen in cirrhosis), vitiligo (loss of skin pigmentation like Michael
Jackson), diabetes mellitus, and adrenal
insufficiency....
Dr. Melissa Palmer Answers Our Questions
Specialty: Gastroenterology and Hepatology
Medical
advisory board of the ALF New York Chapter
ALF
National Chapter Nutrition Education Subcommittee
January
2000
7.)
Have there been any studies done on a connection between pbc and rheumatoid
arthritis?
Answer
Have
there been any studies done on a connection between pbc and rheumatoid arthritis?
Since many rheumatologic disorders have an autoimmune origin, it is not
surprising that there is a high degree of association between
rheumatologicdisorders and PBC. Rhematoid arthritis, which is characterized
by joint aches and joint deformities, is often seen in people with PBC. Other
rheumatologic disorders occurring in people with PBC include Sjogrens syndrome,
which is characterized by dry eyes and dry mouth, scleroderma, characterized
by thickening and hardening of the skin and even some internal organs, and
raynauds phenomenon, that typically causes the fingertips to turn blue and
become numb when exposed to cold weather or emotional stress.
Alfred
L. Baker, M.D.
Division of Gastroenterology & Hepatology
Northwestern Memorial Hospital
Chicago,
IL
Show
2000-2001
1.)
Some Drs. consider PBC to be a systemic disease and it is not a coincidence
that many of us also suffer from other autoimmune diseases/conditions. For
e.g. colitis, IBS, arthritis, sojgrens etc. What are your thoughts?
Answer
PBC
is generally regarded as a multisystem disorder, or a disease that involves
several different organs and systems in the body. The liver is most commonly
involved, but patients frequently have Sjogrens syndrome (dry mouth
and dry eyes due to inflammation of the lacrimal and salivary glands that
moisten the eyes and mouth along with a disorder such as rheumatoid arthritis),
inflammation of the thyroid gland, and difficulty with swallowing because
of involvement of the esophagus. Some patients may have pancreatic involvement,
but this usually causes no symptoms. Occasionally patients may have scleroderma,
a disease that causes thickening of the skin. However, the irritable bowel
syndrome and various forms of colitis are not ordinarily thought to be a
part of the multisystem involvement that often characterizes PBC.
David
Bernstein, M.D.
Chief,
Division of Gastroenterology
North
Shore University Hospital
Manhasset,
NY
July
2000
Question
20:
Why
do people with GERD suffer from chronic cough? Are there any other problems
related to chronic cough and PBC?
Answer 20
GERD
can lead to many effects outside of the esophagus and stomach. Gastroesophageal
reflux commonly leads to chronic cough and hoarseness. The refluxate or gastric
juices pass through the esophagus and enters the trachea and lungs and causes
irritation. The irritation leads to coughing. GERD has even been felt to
be a possible cause of asthma in some patients. This cough is treated with
anti-acid medications.
There
are several chronic pulmonary conditions associated with PBC. PBCers can
develop interstitial pulmonary fibrosis and those with either Sjogren's syndrome
or scleraderma can also develop a chronic cough.